Cerebellar Haemangioblastoma

cerebellar haemangioblastoma

T1-weighted gadolinium-enhanced MRI image in a patient with von Hippel-Lindau disease presenting with type-2 infratentorial hemangioblastomas. The larger tumor shows cystic central areas within.

Intracranial hemangioblastomas can manifest 3 morphologic patterns based on the macroscopic pathology. These are well correlated with the MRI findings and include (1) cyst with a small mural nodule, (2) solid mass with a central cystic component, and (3) solid tumor without a cystic component. A cyst with a small mural nodule is the most common presentation. Solid masses with a central cyst behave similarly; therefore, the different morphologic patterns have been postulated to be part of the natural history of a solid tumor that develops a cystic component around or within it. Solid hemangioblastomas occur less frequently than the other patterns. The lesion is isointense or hypointense on T1-weighted images and hyperintense on T2-weighted images.

Reference: Avila NA, Shawker TH, Choyke PL, Oldfield EH: Cerebellar and spinal hemangioblastomas: evaluation with intraoperative gray-scale color Doppler flow US. Radiology 1993 Jul; 188(1): 143-7.

Credit: Dr Abhijit Datir